Can you live a normal life with Dandy-Walker Syndrome?
The presence of multiple congenital defects may shorten life span. The effect of Dandy-Walker Syndrome on intellectual development is variable, with some children having normal cognition and others never achieving normal intellectual development even when the excess fluid buildup is treated early and correctly.
Can a baby survive with Dandy-Walker Syndrome?
Some people with Dandy-Walker complex may have physical disabilities or intellectual disabilities . In most cases, infants who have isolated Dandy-Walker variant are more likely to have normal outcomes in the newborn period.
Is Dandy-Walker Syndrome fatal?
Rarely, people with Dandy-Walker malformation have no health problems related to the condition. Problems related to hydrocephalus or complications of its treatment are the most common cause of death in people with Dandy-Walker malformation.
Is Dandy-Walker Syndrome a birth defect?
The Dandy-Walker malformation is a congenital (present at birth) defect affecting the cerebellum, the back part of the brain that controls movement, behavior and cognitive ability.
What is a dandy walker baby?
Dandy-Walker Syndrome is a congenital birth defect that in- volves the cerebellum of the brain and the fluid filled spaces around it. The cerebellum, located at the back of the brain, con- trols movement. No gene or cause has yet to be identified but a familial link has been seen.
What causes Dandy Walker syndrome?
In most cases, the exact cause of Dandy-Walker complex is unknown. It is thought that most cases are caused by a combination of genetic and environmental factors that affect early development before birth.
How is Dandy Walker malformation diagnosed?
Dandy Walker malformation is diagnosed with the use of ultrasound, CT and MRI. Prenatal diagnosis of Dandy-Walker malformation is sometimes made by ultrasound or fetal MRI.
How is Dandy Walker diagnosed?
How did Dandy Walker syndrome get its name?
The syndrome is named after physicians Walter Dandy and Arthur Walker, who described associated signs and symptoms of the syndrome in the 1900s. The malformations often develop during embryonic stages.
What is the prognosis for Dandy Walker syndrome?
Prognosis The effect of Dandy-Walker Syndrome on intellectual development is variable, with some children having normal cognition and others never achieving normal intellectual development even when the excess fluid buildup is treated early and correctly. Longevity depends on the severity of the syndrome and associated malformations.
How can you tell if your baby has Dandy Walker syndrome?
The findings on ultrasound consist of a cyst in the cerebellum. There may or may not be other birth defects in the brain or in other organ systems. It is very important to have your fetus evaluated by a physician experienced with DWM, such as a Maternal-Fetal Medicine specialist in order to determine the extent of the birth defect (s).
How many children have Dandy Walker malformation?
Dandy Walker Malformation is sometimes seen with other abnormalities such as cleft palate, enlarged kidneys with cysts, spinal cord defects, and other brain defects. How many children have Dandy Walker Malformation? Dandy Walker Malformation occurs in one out of 25,000 babies, affecting girls more often than boys.
Which is part of the brain does Dandy Walker syndrome affect?
Dandy-Walker Syndrome is a congenital brain malformation involving the cerebellum (an area at the back of the brain that controls movement) and the fluid-filled spaces around it.
Dandy Walker syndrome (DWS) is brought about by an abnormal brain development that caused the cerebellum to become defective or abnormally formed, specifically at the posterior part of the brain.
What causes Dandy Walker?
The cause of Dandy–Walker syndrome is a partial or complete congenital failure of the cerebellar vermis to develop, which blocks the circulation of cerebrospinal fluid.
What is Dandy Walker malformation?
The Dandy-Walker malformation is a congenital (present at birth) defect affecting the cerebellum, the back part of the brain that controls movement, behavior, and cognitive ability.
What is Dandy Walker disease?
Dandy-Walker syndrome, also known as the Dandy-Walker malformation, is a rare, congenital hydrocephalus (a buildup of fluid in the brain) that affects the cerebellum portion of the brain. The condition, which occurs in one in every 25,000 to 35,000 live births each year, causes different parts of the cerebellum to develop abnormally.